An 11-year-old girl presented in hemolytic crisis with fulminant hepatic failure requiring liver transplantation. Viral serologies were negative. The serum ceruloplasmin level was 4.2 mg/dL (low). The explanted liver weighed 984 g and was diffusely nodular. No discrete masses were identified. A PAS with diastase histochemical stain was negative in the liver.
The master list with the correct answer
• Acetaminophen toxicity
• Alpha-1 antitrypsin deficiency
• Nodular regenerative hyperplasia
• Primary biliary cirrhosis
• Viral hepatitis
• Wilson disease
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• Appropriate diagnosis
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